Abstract: Objective　To retrospectively analyze the clinical characteristics of incomplete kawasaki disease（IKD） with coronary artery aneurysms（CAA）．Methods　From the 997 children with KD treated in Xi'an Children's Hospital between January 2012 and June 2017，we enrolled all the children with IKD and CAA（n=22，IKD+CAA group），all the children with complete kawasaki disease（CKD） and CAA（n=36，CKD+CAA group），and 116 with CKD and normal coronary artery（NCA） （randomly sampled from other 939 cases）．We collected their epidemiological data〔sex，age of onset，duration of suffering from fever，onset season，place of residence（urban/rural area）〕，laboratory data〔white cell count（WBC），hemoglobin（Hb），neutrophils（N），platelet （PLT），albumin （ALB），alanine aminotransferase （ALT），aspartate aminotransferase（AST），calcitonin（PCT） and fibrinogen（FIB）〕 and other data such as prevalence rates of mycoplasma（MP） and EB virus（EBV） infection.Results　Male patients outnumbered female patients，and rural patients outnumbered urban patients in both IKD+CAA and CKD+CAA groups．In both CKD+CAA and CKD+NCA groups，more patients had an onset age of ≥1 rather than < 1，more patients owned a history of suffering from fever < 10 days instead of ≥10 days，and more patients were attacked in summer than in other seasons．All groups showed similar baseline levels of WBC，Hb，N，PLT，ALB，ALT，AST，ESR，PCT，and FIB（P>0.05）．The prevalence rates of MP infection were 9.1%，16.7%，22.4% in IKD+CAA group，CKD+CAA group and CKD+NCA group，respectively.Furthermore，the prevalence rates of EBV infection were 4.5%，8.3%，4.3% in IKD+CAA group，CKD+CAA group and CKD+NCA group，respectively.Conclusion　Men and those from rural areas were more susceptible to IKD combined with CAA.The laboratory values were similar in IKD+CAA group，CKD+CAA group and CKD+NCA group.In addition，the detection of CAA should be strengthened in those with an increased duration of fever，a younger age of onset，or suspected IKD.

Key words: Mucocutaneous lymph node syndrome, Coronary aneurysm, Disease attributes

摘要： 目的　回顾性分析不完全川崎病（IKD）合并冠状动脉瘤（CAA）（以下简称IKD+CAA）的临床特点。方法　选取2012年1月—2017年6月西安市儿童医院收治的川崎病（KD）患儿997例，其中IKD+CAA患儿22例（IKD+CAA组），完全川崎病（CKD）合并CAA患儿36例（CKD+CAA组），在剩余939例患儿中随机抽取CKD合并冠状动脉正常（NCA）患儿116例（CKD+NCA组）。收集3组患儿的流行病学资料〔性别、年龄（<1岁及≥1岁）、热程（<10 d及≥10 d）、发病季节、区域（城市、农村）〕、实验室检查资料〔白细胞计数（WBC）、血红蛋白（Hb）、中性粒细胞计数（N）、血小板计数（PLT）、清蛋白（ALB）、谷氨酸氨基转移酶（ALT）、天冬氨酸氨基转移酶（AST）、降钙素原（PCT）、纤维蛋白原（FIB）〕及支原体（MP）、EB病毒（EBV）感染资料。结果　IKD+CAA组、CKD+CAA组男性比例高于女性；CKD+CAA组、CKD+NCA组发病年龄≥1岁比例高于年龄<1岁；CKD+CAA组、CKD+NCA组热程<10 d比例高于热程≥10 d；CKD+CAA组、CKD+NCA组夏季发病率高于其他季节；IKD+CAA组、CKD+CAA组农村发病比例高于城市。3组患儿WBC、Hb、N、PLT、ALB、ALT、AST、ESR、PCT、FIB比较，差异无统计学意义（P>0.05）。IKD+CAA患儿MP感染比例为9.1%，CKD+CAA患儿MP感染比例为16.7%，CKD+NCA患儿MP感染比例为22.4%；IKD+CAA患儿EBV感染比例为4.5%，CKD+CAA患儿EBV感染比例为8.3%，CKD+NCA患儿EBV感染比例为4.3%。结论　IKD+CAA以男性为主，农村发病比例高于城市，实验室检查结果与CKD+CAA、CKD+NCA无差异，临床上对于热程长、年龄小、疑诊IKD的患儿要加强冠状动脉的监测。

关键词: 黏膜皮肤淋巴结综合征, 冠状动脉瘤, 疾病特征