Malignant Perivascular Epithelioid Cell Tumor of the Uterus：a Case Report and Literature Review

doi:10.12114/j.issn.1007-9572.2021.00.001

Abstract

Abstract: Malignant perivascular epithelioid cell tumor （PEComa） of the uterus is a rare gynecologic tumor，which is easy to be misdiagnosed before operation.We retrospectively analyzed the clinical data，imaging presentations and pathological characteristics of a patient with PEComa of the uterus，and reviewed available studies about the disease，in order to improve the knowledge of the disease among medical workers.

Key words: Perivascular epithelioid cell neoplasms, Uterus, Malignant tumor, Case reports

摘要： 子宫恶性血管周上皮样细胞肿瘤（PEComa）是一种罕见的妇科肿瘤，术前易误诊。本文通过回顾性分析1例诊断为子宫颈恶性PEComa患者的临床资料、影像学表现及病理特点，结合目前子宫恶性PEComa的研究进展进行文献复习，以提高广大医务工作者对该疾病的认识。

关键词: 血管周上皮样细胞肿瘤, 子宫, 恶性肿瘤, 病例报告

ZHENG Yongfei,ZHENG Hailan,WANG Sheng, et al. Malignant Perivascular Epithelioid Cell Tumor of the Uterus：a Case Report and Literature Review　[J]. Chinese General Practice, 2021, 24(18): 2364-2367. DOI: 10.12114/j.issn.1007-9572.2021.00.001.
郑永飞,郑海澜,汪晟等. 子宫恶性血管周上皮样细胞肿瘤一例报道并文献复习[J]. 中国全科医学, 2021, 24(18): 2364-2367. DOI: 10.12114/j.issn.1007-9572.2021.00.001.

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