EBV-associated Hemophagocytic Syndrome：a Case Report and Literature Review

doi:10.12114/j.issn.1007-9572.2019.00.480

Abstract

Abstract: Hemophagocytic syndrome is a rare histocyte disease in children.Due to lack of specific clinical manifestations in the early stage，it is very easily misdiagnosed，delaying the appropriate treatment.We retrospectively analyzed the clinical data and treatment of one child with EBV-associated hemophagocytic syndrome，and reviewed available studies about the disease，to help clinical workers identify hemophagocytic syndrome at an early stage，by which the survival opportunities in such patients can be increased.

Key words: Lymphohistiocytosis, hemophagocytic；Herpesvirus 4, human；Epstein-Barr virus；Child；Case reports

摘要： 噬血细胞综合征是儿童少见的组织细胞疾病，早期表现缺乏特异性，极易造成误诊，延误治疗机会。本文通过回顾性分析1例诊断为EB病毒相关性噬血细胞综合征（EBV-HLH）患儿的临床资料、治疗情况，结合目前EBV-HLH的研究进展进行文献复习，以便临床工作者早期识别嗜血细胞综合征，为患儿争取生存机会。
淋巴组织细胞增多症，嗜血细胞性；疱疹病毒4型，人；EB病毒；儿童；病例报告

WANG Jiangya,SUN Meng,ZHENG Youning. EBV-associated Hemophagocytic Syndrome：a Case Report and Literature Review　[J]. Chinese General Practice, 2020, 23(11): 1445-1448. DOI: 10.12114/j.issn.1007-9572.2019.00.480.
王江娅,孙萌,郑有宁. EB病毒相关性噬血细胞综合征一例报道并文献复习[J]. 中国全科医学, 2020, 23(11): 1445-1448. DOI: 10.12114/j.issn.1007-9572.2019.00.480.

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